TopicNeuroscience

lysosomal storage disorders

Content Overview
5Total items
4ePosters
1Seminar

Latest

SeminarNeuroscience

Lysosomal storage disorders and their unanticipated links to rare and common diseases

Frances Platt
University of Oxford
Feb 8, 2021

Lysosomal storage diseases are a group of over 70 inherited metabolic disorders, many of which have a neurodegenerative clinical course. Treatments have been developed for a subset of these disorders and are now in routine clinical use. We have found that some neurological and neurodegenerative diseases share unanticipated links to lysosomal storage diseases providing insights into disease pathogenesis. These links also suggest treatments developed for lysosomal disorders may have unanticipated utility in other rare and common diseases.

ePosterNeuroscience

Common patterns of schizophrenia and lysosomal storage disorders

Anastasia Bezrukova, Katerina Basharova, Mikhail Nikolaev, Ekaterina Palchikova, Irina Miliukhina, Galina Baydakova, Natalia Zalutskaya, Ekaterina Zakharova, Sofya Pchelina, Tatiana Usenko
ePosterNeuroscience

Developmental delay in striatal synaptic pruning in lysosomal storage disorders

Mariagrazia Monaco, Cristina Somma, Alessandro Nicois, Maria de Risi, Luigia Cristino, Elvira de Leonibus

FENS Forum 2024

ePosterNeuroscience

Dopaminergic treatments for autistic-like behaviour in lysosomal storage disorders: Preclinical and clinical evidence

Maria De Risi, Lorenzo Cusimano, Xabier Bujanda Cundin, Mariateresa Pizzo, Simona Fecarotta, Giancarlo Parenti, Elvira De Leonibus

FENS Forum 2024

ePosterNeuroscience

Pharmacological stimulation of autophagy to rescue proteinopathy and cognitive decline in lysosomal storage disorders

Cristina Somma, Mariagrazia Monaco, Antonella Capuozzo, Diego Luis Medina, Maria de Risi, Elvira de Leonibus

FENS Forum 2024

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